Congenital adrenal hyperplasia

(Mnemonic: 17 + 3 = ~21; 11)

1. 17α-hydroxylase

2. 3β-HSD

3. 21-hydroxylase (m/c type of CAH)

4. 11β-hydroxylase

HSD – Hydroxysteroid dehydrogenase

 

Ambiguous genitalia

in female

Under virilized male

(Testosterone not

synthesis)

Salt wasting and

Hyperkalemia

21-hydroxylase deficiency

3β-HSD

Hypertension

(HTN)

11β-hydroxylase deficiency 

(INICET May 2024)

17α-hydroxylase deficiency 

 

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